Beta-ureidopropionase is an enzyme involved in the final step of pyrimidine catabolism, converting N-carbamoyl-beta-alanine and N-carbamoyl-beta-aminoisobutyric acid into beta-alanine and beta-aminoisobutyric acid, respectively. Deficiency in this enzyme can lead to neurological symptoms and is associated with a rare metabolic disorder known as beta-ureidopropionase deficiency.